Deletion of the protein tyrosine phosphatase gene PTPN2 in T-cell acute lymphoblastic leukemia

Nat Genet. 2010 Jun;42(6):530-5. doi: 10.1038/ng.587. Epub 2010 May 16.

Abstract

PTPN2 (protein tyrosine phosphatase non-receptor type 2, also known as TC-PTP) is a cytosolic tyrosine phosphatase that functions as a negative regulator of a variety of tyrosine kinases and other signaling proteins. In agreement with its role in the regulation of the immune system, PTPN2 was identified as a susceptibility locus for autoimmune diseases. In this work, we describe the identification of focal deletions of PTPN2 in human T-cell acute lymphoblastic leukemia (T-ALL). Deletion of PTPN2 was specifically found in T-ALLs with aberrant expression of the TLX1 transcription factor oncogene, including four cases also expressing the NUP214-ABL1 tyrosine kinase. Knockdown of PTPN2 increased the proliferation and cytokine sensitivity of T-ALL cells. In addition, PTPN2 was identified as a negative regulator of NUP214-ABL1 kinase activity. Our study provides genetic and functional evidence for a tumor suppressor role of PTPN2 and suggests that expression of PTPN2 may modulate response to treatment.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Benzamides
  • Cell Line
  • Cell Line, Tumor
  • Chemokine CCL1 / metabolism
  • Gene Deletion*
  • Gene Knockdown Techniques
  • Homeodomain Proteins / genetics
  • Humans
  • Imatinib Mesylate
  • Interleukin-2 / metabolism
  • Interleukin-7 / metabolism
  • Leukemia, Experimental / genetics
  • Mice
  • Piperazines / therapeutic use
  • Precursor T-Cell Lymphoblastic Leukemia-Lymphoma / genetics*
  • Protein Tyrosine Phosphatase, Non-Receptor Type 2 / genetics*
  • Proto-Oncogene Proteins / genetics
  • Pyrimidines / therapeutic use

Substances

  • Benzamides
  • Chemokine CCL1
  • Homeodomain Proteins
  • Interleukin-2
  • Interleukin-7
  • Piperazines
  • Proto-Oncogene Proteins
  • Pyrimidines
  • TLX1 protein, human
  • Imatinib Mesylate
  • PTPN2 protein, human
  • Protein Tyrosine Phosphatase, Non-Receptor Type 2

Associated data

  • RefSeq/NM_002828
  • RefSeq/NM_008977
  • RefSeq/NM_080422
  • RefSeq/NM_080423